Abstract
Objective
The purpose of this study was to report the clinical characteristics and long-term
visual outcomes in a cohort of children with idiopathic intracranial hypertension
(IIH).
Design
Retrospective, observational cohort study.
Participants
Consecutive children who met the diagnostic criteria for definite IIH at a tertiary
care pediatric hospital between 2009 and 2020.
Methods
The charts of pediatric patients with IIH were reviewed. The main outcome measure
was long-term visual impairment, with an analysis of clinical features by age and
risk factors for a poor visual outcome.
Results
There were 110 children (75 females) with IIH. At presentation, younger children with
IIH were less likely to present with headaches (p = 0.01) and more likely to be asymptomatic (p = 0.03). There was a strong association with female sex (p < 0.001) and higher body mass index (p < 0.001) in adolescents in comparison to younger children. Of the 90 patients with
long-term visual outcome data, only 8 (9%) had evidence of mild visual impairment
(1 loss of visual acuity, 7 loss of visual field) with no cases of severe visual impairment.
On risk factor analysis, the only variable associated with a poor visual outcome was
greater severity of papilledema at diagnosis.
Conclusions
In this large series of pediatric IIH, the long-term visual outcomes were favourable,
with evidence of mild visual impairment in less than 10% of patients.
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Article Info
Publication History
Published online: July 17, 2021
Accepted:
June 15,
2021
Received in revised form:
May 20,
2021
Received:
April 1,
2021
Publication stage
In Press Corrected ProofFootnotes
The abstract has been accepted for presentation at the 2021 Virtual Meeting of the American Association of Pediatric Ophthalmology and Strabismus (AAPOS).
Identification
Copyright
© 2021 Canadian Ophthalmological Society. Published by Elsevier Inc. All rights reserved.
