A 25-year-old male patient presented with biopsy-proven Alport's syndrome with bilateral
cataracts (history of unstable refractive error over past 6 years with recent-onset
diminution of vision in either eye for the past 1 year; best-corrected visual acuities
of 20/100 OD and 20/200 OS; (Fig. 1A, B). On optical coherence tomography the patient showed right eye lenticonus (Fig. 1C) with a communicating hyperreflectivity (fibrosed hydration track) between the anterior
capsular and subcapsular opacities (Fig. 2A). The left eye showed a flatter anterior curvature with hyperreflective dots in
the anterior chamber suggestive of leaked lens matter or low-grade inflammation (Fig. 1D) with volume loss in the anterior subcapsular region (Fig. 2B) and a localized area of capsular thinning (Fig. 2C). It was hypothesized that microruptures in the anterior capsule (secondary to thinning
in the lenticonus) with aqueous hydration could have caused the bilateral cataract
and lenticular volume loss in the left eye, thus called hydrops.
To read this article in full you will need to make a payment
Purchase one-time access:
Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online accessOne-time access price info
- For academic or personal research use, select 'Academic and Personal'
- For corporate R&D use, select 'Corporate R&D Professionals'
Subscribe:
Subscribe to Canadian Journal of OphthalmologyAlready a print subscriber? Claim online access
Already an online subscriber? Sign in
Register: Create an account
Institutional Access: Sign in to ScienceDirect
Article info
Publication history
Published online: August 12, 2022
Accepted:
July 19,
2022
Received in revised form:
June 19,
2022
Received:
May 18,
2022
Identification
Copyright
© 2022 Canadian Ophthalmological Society. Published by Elsevier Inc. All rights reserved.
