A 56-year-old white male patient was referred for management of a choroidal mass in his left eye. A cutaneous nevus flammeus involving the right side of his face extending to the right side of his neck and upper chest was noticed (Fig. 1A). On questioning, he mentioned that this nevus flammeus was previously treated with several sessions of dye laser. In addition, the eyelid skin showed a blue-grey hue that involved the upper and lower eyelids bilaterally (Fig. 1B, C). Slit-lamp examination revealed bilateral multiple flat, purple-coloured episcleral patches.