Correspondence
Primary intraocular malignant rhabdoid tumor presenting as orbital mass with intracranial extension in an adolescent
A malignant rhabdoid tumor (MRT) is a highly aggressive tumour of the kidney. Extra renal MRTs have also been described as cytologically resembling renal rhabdoid tumours and are known to be highly lethal with a poor prognosis. Orbital presentation of MRT was first reported by Rootman et al. in 1989.1 Since then, a few MRTs of the orbit have been reported in infants, but none as a primary intraocular MRT presenting as an orbital mass in adolescents.
