Chordomas are rare neoplasms derived from primitive notochordal remnants that almost always develop from bone and that can occur anywhere along the spinal axis from the clivus to the sacrum.1,2 Fifty percent of these tumours occur in the sacrococcygeal area, 35% arise from the clivus, and 15% arise elsewhere in the vertebral column.3 Skull base chordomas account for 0.3%–1.0% of intracranial tumours.4 Chordomas can develop at any age, but they typically affect patients in the third, fourth, and fifth decades of life.
